The case notes of 200 patients with cryptogenic fibrosing alveolitis, from three regions in the United Kingdom, were reviewed, in order to determine how physicians manage this uncommion condition.
In the majority of cases (119), the diagnosis was based solely on clinical grounds, with no attempt at histological confirmation of the diagnosis.
Transbronchial biopsy was attempted in 66 patients, but was unhelpful in confirming a diagnosis of pulmonary fibrosis in 30% of these patients.
Thirty five patients underwent bronchoalveolar lavage, and 15 had an open lung biopsy.
Of the 132 patients treated, 110 received prednisolone alone, and the rest a combination of other unmunosuppressive agents.
Mots-clés Pascal : Pneumopathie interstitielle, Royaume Uni, Europe, Idiopathique, Homme, Appareil respiratoire pathologie, Diagnostic, Traitement, Biopsie, Lavage bronchoalvéolaire, Poumon pathologie, Epidémiologie, Exploration
Mots-clés Pascal anglais : Interstitial pneumonitis, United Kingdom, Europe, Idiopathic, Human, Respiratory disease, Diagnosis, Treatment, Biopsy, Bronchoalveolar lavage, Epidemiology, Exploration
Notice produite par :
Inist-CNRS - Institut de l'Information Scientifique et Technique
Cote : 93-0571371
Code Inist : 002B11C. Création : 199406.