Pulmonary alveolar microlithiasis is a rare disorder, only 173 cases having been reported worldwide.
Fifty two cases from Turkey are reported, 49 of witch have previously been described only in Turkish publications.
The mean age of the patients was 27 (SD 12) years, 34 were male, and 10 were symptomless.
In 40 of the 52 cases diagnosis was confirmed histopatologically.
Nineteen cases were diagnosed in siblings.
This high rate suggests that pulmonary alveolar microlithiasis is a familial disease, which, though rare, is for unknown reasons most common in Turkey.
Mots-clés Pascal : Appareil respiratoire pathologie, Epidémiologie, Exploration, Homme, Microlithiase, Alvéole pulmonaire, Turquie, Asie
Mots-clés Pascal anglais : Respiratory disease, Epidemiology, Exploration, Human, Microlithiasis, Pulmonary alveolus, Turkey, Asia
Notice produite par :
Inist-CNRS - Institut de l'Information Scientifique et Technique
Cote : 93-0333201
Code Inist : 002B11C. Création : 199406.