The Latin American Group for Primary Immunodeficiencies, formed in 1993, presently includes 12 countries.
One goal was to study the frequency of primary immunodeficiencies in various regions of the American continent and to enhance knowledge about these diseases among primary-care physicians, as well as allergist-immunologists.
Important for this purpose was the development of a registry of primary immunodeficiencies using a uniform questionnaire and computerized database.
To date, eight countries have collected information on a total of 1428 patients.
Predominantly antibody deficiencies were reported in 58% of patients, followed by cellular and antibody immunodeficiencies associated with other abnormalities in 18%, immunodeficiency syndromes associated with granulocyte dysfunction in 8%, phagocytic disorders in 9%, combined cellular and antibody immunodeficiencies in 5%, and complement deficiencies in 2% of patients.
The information gathered from this initial analysis of data will serve to expand the patient database to more areas within participating countries and to new countries and to increase collaboration toward better diagnosis and treatment of these diseases.
Mots-clés Pascal : Immunodéficit, Primaire, Epidémiologie, Amérique Latine, Amérique, Registre, Questionnaire, Base donnée, Assistance ordinateur, Homme, Immunopathologie, Informatique biomédicale
Mots-clés Pascal anglais : Immune deficiency, Primary, Epidemiology, Latin America, America, Register, Questionnaire, Database, Computer aid, Human, Immunopathology, Biomedical data processing
Notice produite par :
Inist-CNRS - Institut de l'Information Scientifique et Technique
Cote : 98-0202433
Code Inist : 002B06D01. Création : 11/09/1998.