Moyamoya disease in the United States.
Copyright (c) 1997 Elsevier Science B.V. All rights reserved.
The epidemiology and radiological features of Moyamoya disease (MMD) in the US were investigated.
This study encompassed 98 cases ; 26 were newly collected from eight US institutions and 72 were previously reported in the US literature.
The patients ranged in age from 6 months to 67 years with age peaks in the first, third and fourth decades.
MMD was seen in various ethnic groups and females were more commonly involved (71%) than males.
A specific etiology could not be determined in most cases but arteriosclerosis and use of oral contraceptives were occasional associations.
On angiography and/or magnetic resonance angiography (MRA), carotid arterial stenosis or occlusion was seen bilaterally in 95 cases (97%) and unilaterally in three.
On MR or MRA, internal carotid steno-occlusive lesions were well demonstrated in all cases but Moyamoya collateral vessels (MMVs) were visualized in only 65% of the patients.
MMVs in the basal ganglia and thalami were best demonstrated on T1 weighted images.
Parenchymal lesions were seen in all patients and were often bilateral.
With advances in MR techniques and increasing awareness of diagnostic guidelines, MMD will be diagnosed more frequently than before in the US 1997 Elsevier Science B.V.
Mots-clés Pascal : Nishimoto Kudo maladie, Etats Unis, Amérique du Nord, Amérique, Age, Ethnie, Angiographie RMN, Carotide, Epidémiologie, Diagnostic, Homme, Encéphale pathologie, Système nerveux central pathologie, Système nerveux pathologie, Vaisseau sanguin pathologie, Appareil circulatoire pathologie, Cérébrovasculaire pathologie, Imagerie RMN, Imagerie médicale
Mots-clés Pascal anglais : Nishimoto Kudo disease, United States, North America, America, Age, Ethnic group, NMR angiography, Carotid, Epidemiology, Diagnosis, Human, Cerebral disorder, Central nervous system disease, Nervous system diseases, Vascular disease, Cardiovascular disease, Cerebrovascular disease, Nuclear magnetic resonance imaging, Medical imagery
Notice produite par :
Inist-CNRS - Institut de l'Information Scientifique et Technique
Cote : 98-0006954
Code Inist : 002B17C. Création : 17/04/1998.