Vasculitis in familial Mediterranean fever.
To evaluate the frequency of vasculitis, mainly in the forms of Henoch-Schönlein purpura and polyarteritis nodosa (PAN), and to investigate the presence of occult blood in the first stool specimens after an abdominal attack in Turkish patients with familial Mediterranean fever (FMF).
Review of the charts of 207 patients with FMF seen between 1983 and 1993 with respect to clinical vasculitis.
A prospective study designed to test the presence of occult blood in the first stool specimens obtained after abdominal attack and at least one week later in 36 patients with FMF compared with healthy and diseased controls.
There were 15 patients with Henoch-Schönlein purpura (7%), 2 with definite and one with probable PAN (1%), one of whom developed perirenal hematoma.
The diagnosis of FMF was made after the onset of Henoch-Schönlein purpura in 9 and subsequent to the development of PAN in one patient.
Occult blood was positive in the first stool specimens obtained after an attack in 17 of the 36 patients with FMF (47%), a finding not reported previously.
Vasculitis seems to be an important but not a widely recognized feature of FMF.
Mots-clés Pascal : Purpura rhumatoïde, Homme, Turquie, Asie, Périartérite noueuse, Association, Polysérite familiale récidivante, Epidémiologie, Fréquence, Vascularite, Peau pathologie, Appareil circulatoire pathologie, Vaisseau sanguin pathologie, Capillaire sanguin pathologie, Système ostéoarticulaire pathologie, Maladie système
Mots-clés Pascal anglais : Henoch-Schönlein purpura, Human, Turkey, Asia, Periarteritis nodosa, Association, Familial recurrent polyseritis, Epidemiology, Frequency, Vasculitis, Skin disease, Cardiovascular disease, Vascular disease, Capillary vessel disease, Diseases of the osteoarticular system, Systemic disease
Notice produite par :
Inist-CNRS - Institut de l'Information Scientifique et Technique
Cote : 97-0187322
Code Inist : 002B12B03. Création : 21/05/1997.